##gff-version 3 Q9Y6N1 UniProtKB Transit peptide 1 75 . . . Note=Mitochondrion;Ontology_term=ECO:0000255;evidence=ECO:0000255 Q9Y6N1 UniProtKB Chain 76 276 . . . ID=PRO_0000006080;Note=Cytochrome c oxidase assembly protein COX11%2C mitochondrial Q9Y6N1 UniProtKB Topological domain 76 97 . . . Note=Mitochondrial matrix;Ontology_term=ECO:0000305;evidence=ECO:0000305|PubMed:15229189;Dbxref=PMID:15229189 Q9Y6N1 UniProtKB Transmembrane 98 120 . . . Note=Helical;Ontology_term=ECO:0000255;evidence=ECO:0000255 Q9Y6N1 UniProtKB Topological domain 121 276 . . . Note=Mitochondrial intermembrane;Ontology_term=ECO:0000305;evidence=ECO:0000305|PubMed:15229189;Dbxref=PMID:15229189 Q9Y6N1 UniProtKB Region 64 92 . . . Note=Disordered;Ontology_term=ECO:0000256;evidence=ECO:0000256|SAM:MobiDB-lite Q9Y6N1 UniProtKB Binding site 217 217 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P19516 Q9Y6N1 UniProtKB Binding site 219 219 . . . Ontology_term=ECO:0000250;evidence=ECO:0000250|UniProtKB:P19516 Q9Y6N1 UniProtKB Alternative sequence 217 276 . . . ID=VSP_046360;Note=In isoform 2. CFCFEEQRLNPQEEVDMPVFFYIDPEFAEDPRMIKVDLITLSYTFFEAKEGHKLPVPGYN->ASKLHRVYVLESWHL;Ontology_term=ECO:0000303;evidence=ECO:0000303|PubMed:15489334;Dbxref=PMID:15489334 Q9Y6N1 UniProtKB Natural variant 74 74 . . . ID=VAR_048831;Note=P->L;Dbxref=dbSNP:rs34080917 Q9Y6N1 UniProtKB Natural variant 244 244 . . . ID=VAR_088428;Note=In MC4DN23%3B uncertain significance%3B decreases respiration-derived ATP levels in patient cells. A->P;Ontology_term=ECO:0000269;evidence=ECO:0000269|PubMed:36030551;Dbxref=dbSNP:rs1269413739,PMID:36030551 Q9Y6N1 UniProtKB Natural variant 247 247 . . . ID=VAR_091086;Note=In MC4DN23%3B uncertain significance. P->T;Ontology_term=ECO:0000269;evidence=ECO:0000269|PubMed:38068960;Dbxref=dbSNP:rs2509376984,PMID:38068960 Q9Y6N1 UniProtKB Sequence conflict 187 187 . . . Note=A->V;Ontology_term=ECO:0000305;evidence=ECO:0000305 Q9Y6N1 UniProtKB Sequence conflict 223 223 . . . Note=V->G;Ontology_term=ECO:0000305;evidence=ECO:0000305